Hand Schuller Christian Disease: A Rare Case Report with Oral Manifestation
Published: January 1, 2015 | DOI: https://doi.org/10.7860/JCDR/2015/.5481
Ch. Lalitha, M. Manjula, K. Srikant, Stuti Goyal, Shahela Tanveer
1. Senior Lecturer, Department of Oral Medicine and Radiology, Sri Sai College of Dental Surgery, Vikarabad, Telanagana, India, India.
2. Professor, Department of Oral Medicine and Radiology, Gandhi Hospitals, Hyderabad, India.
3. Senior Lecturer, Department of Oral Medicine and Radiology, Sri Sai College of Dental Surgery, Vikarabad, India.
4. Senior Lecturer, Department of Oral Medicine and Radiology, Sri Sai College of Dental Surgery, Vikarabad, India.
5. Senior Lecturer, Department of Oral Pathology, Sri Sai College of Dental Surgery, Vikarabad, India.
Correspondence
Dr. Ch. Lalitha,
Senior Lecturer, Sri Sai College of Dental Surgery, Vikarabad, Telanagana, India.
E-mail: dr.lalithaomr@gmail.com
Langerhan’s Cell Histiocytosis (LCH) is disorders which include abnormalities that result from abnormal proliferation of langerhan’s cells or their precursors. LCH is clinically classified into three types-eosinophilic granuloma, Hand Schuller Christian disease and Abt-Letterer- Siwe disease. It is usually manifested in childhood as well as in adulthood. The clinical manifestations are the result of the accumulation and infilteration of the langerhan cells in organs and tissues. Here is a rare case report of 6-year-old boy with extraoral manifestation of exopthalmic right eye and oral manifestation of mobility of teeth and with typical radiological findings. Basing on the clinical, radiological and histopathological examination the diagnosis of Hand Schuller Christian Disease was given.
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